Huntington's disease (HD) accounts for around 90% of cases of chorea of genetic etiology, but a number of other distinct genetic disorders can present with a clinical picture indistinguishable from HD. In this article, Schneider et al. review the clinical features and genetic bases of these HD-like syndromes, discussing the clinical clues that should prompt further investigations in patients presenting with these conditions.
- Susanne A Schneider
- Ruth H Walker
- Kailash P Bhatia